SMA的病程評估是依照其年齡以及可執行的功能來選擇合適的運動功能量表及電生理檢測^1-3

許多運動功能評估量表已發展，證明可在多種條件下使用，包括^3-5：

臨床研究中對脊髓性肌肉萎縮症自然病史的評估
建立一基準線，以在臨床試驗中觀察試驗藥物對於運動功能的潛在好處

^*以下非完整的評估量表，僅供參考

→	CHOP INTEND
→	HFMSE
→	HINE
→	ULM、RULM
→	6MWT
→	CMAP、MUNE

影響各運動功能評估準確性的因素

若評估者有感患者變化，卻未反應在分數上，則可再次檢查下列可能的影響因素。此外，評估時的陪同者、病人的配合度、過程中是否給予標準正向回饋、評估時間是否符合生理作息以及是否有適當的休息，都可能對評估結果造成影響。

現有運動功能評估工具的挑戰與展望

SMA 疾病表現隨醫療積極介入後有極大改變，

評估 SMA 患者的方式也需與時俱進27。

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REFERENCES

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SMA患者的基本活動能力與病情進展如何決定日常活動與生活方式？